creators_name: Shakuntala, PN
creators_name: Poornima, M
creators_name: Padmalatha, VV
creators_name: Rao, SR
creators_id: shakuntala_pn@yahoo.com
editors_name: Kakkilaya, Srinivas
editors_id: Kakkilaya BS
type: journale
datestamp: 2013-05-04 23:08:47
lastmod: 2013-05-04 23:08:47
metadata_visibility: show
title: Successful Pregnancy Outcome In Maternal Crigler Najjar Syndrome Type II.
ispublished: pub
subjects: OJHAS
full_text_status: public
keywords: Crigler Najjer Syndrome type II; Unconjugated hyperbilurubinemia; Phenobarbitone; Phototherapy.
abstract: Estimated incidence of Crigler-Najjar syndrome(CNS) is 1 case per 1,000,000 births(1 million). The overall prevalence of CN syndrome is unknown, with only several hundred people reported to have this disease. It is interestingly very rare to encounter a pregnant adult women with congenital jaundice. Pregnancy in CN type II patients is a diagnostic and a therapeutic challenge because of the high risk of bilirubin encephalopathy with serious neurological damage as life-threatening complications for the fetus. To date 8 pregnancy outcome have been reported from 5 women and we report the6 woman with a successful 9 th pregnancy outcome. We have discussed detail history, presentation and management during pregnancy and care of the new born.
date: 2012-10-25
date_type: published
publication: Online Journal of Health and Allied Sciences
volume: 11
number: 3(12)
publisher: Kakkilaya BS
refereed: TRUE
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citation:   Shakuntala, PN and Poornima, M and Padmalatha, VV and Rao, SR  (2012) Successful Pregnancy Outcome In Maternal Crigler Najjar Syndrome Type II.  [Journal (On-line/Unpaginated)]     
document_url: http://cogprints.org/8922/1/2012-3-12.pdf