--- abstract: 'Retinal dysplasia represents a congenital disorder characterized by abnormal proliferation of retinal tissue causing leukocoria. We present a case of an infant with bilateral leukocoria, clinically diagnosed as retinoblastoma, followed by enucleation of the left eye. Microscopy however, demonstrated retinal dysplasia consisting of a disorderly proliferation of retinal tissue with formation of rosettes, mimicking retinoblastoma. Microscopic features that aid in differentiating this lesion from retinoblastoma are discussed.' altloc: - http://www.ojhas.org/issue43/2012-3-10.htm chapter: ~ commentary: ~ commref: ~ confdates: ~ conference: ~ confloc: ~ contact_email: ~ creators_id: - drravikumar@metropolisindia.com - ~ - ~ - ~ creators_name: - family: Ravikumar given: HN honourific: '' lineage: '' - family: Vani given: R honourific: '' lineage: '' - family: Santosh given: KV honourific: '' lineage: '' - family: Joji given: A honourific: '' lineage: '' date: 2012-10-25 date_type: published datestamp: 2013-05-04 23:08:39 department: ~ dir: disk0/00/00/89/20 edit_lock_since: ~ edit_lock_until: 0 edit_lock_user: ~ editors_id: - Kakkilaya BS editors_name: - family: Kakkilaya given: Srinivas honourific: Dr lineage: '' eprint_status: archive eprintid: 8920 fileinfo: /style/images/fileicons/application_pdf.png;/8920/1/2012-3-10.pdf full_text_status: public importid: ~ institution: ~ isbn: ~ ispublished: pub issn: ~ item_issues_comment: [] item_issues_count: ~ item_issues_description: [] item_issues_id: [] item_issues_reported_by: [] item_issues_resolved_by: [] item_issues_status: [] item_issues_timestamp: [] item_issues_type: [] keywords: Retinal Dysplasia; Retinoblastoma; Leukocoria lastmod: 2013-05-04 23:08:39 latitude: ~ longitude: ~ metadata_visibility: show note: ~ number: 3(10) pagerange: ~ pubdom: TRUE publication: Online Journal of Health and Allied Sciences publisher: BS Kakkilaya refereed: TRUE referencetext: "1.\tReese AB, Blodi FC: Retinal dysplasia. Am J Ophthalmol 1950;33:23.\r\n2.\tChan A, Lakshminrusimha S, Heffner R, Gonzalez-Fernandez F. Histogenesis of retinal dysplasia in trisomy 13. Diagn Pathol. 2007;2:48.\r\n3.\tde Graaf P, van der Valk P, Moll AC, Imhof SM, Schouten-van Meeteren AY, Castelijns JA. Retinal dysplasia mimicking intraocular tumor: MR imaging findings with histopathologic correlation. AJNR Am J Neuroradiol.2007;28(9):1731-1733.\r\n4.\tLloyd IC, Colley A, Tullo AB, Bonshek R. Dominantly inherited unilateral retinal dysplasia. Br J Ophthalmol. 1993;77(6):378-80.\r\n5.\tAgarwal N, Gupta P, Agarwal A, Pantola C. Retinal Dysplasia – A Mimic of Malignant Ocular Pathology. J of Clinical and Diagnostic Research. 2011:5(2);367-368.\r\n6.\tGonzalez-Fernandez F, Lopes MB, Garcia-Fernandez JM, Foster RG, De Grip WJ, Rosemberg S, Newman SA, VandenBerg SR. Expression of developmentally defined retinal phenotypes in the histogenesis of retinoblastoma. Am J Pathol. 1992;141(2):363-375.\r\n7.\tEagle EC. Ch 11, Retinoblastoma and other pediatric intraocular tumors. In Eye Pathology – An Atlas and Basic Text. W.B. Saunders Co., Philadelphia. 1999. p. 199-205." relation_type: [] relation_uri: [] reportno: ~ rev_number: 9 series: ~ source: ~ status_changed: 2013-05-04 23:08:39 subjects: - OJHAS succeeds: ~ suggestions: ~ sword_depositor: ~ sword_slug: ~ thesistype: ~ title: Retinal Dysplasia Mimicking Retinoblastoma. type: journale userid: 4338 volume: 11