TY - GEN ID - cogprints4279 UR - http://cogprints.org/4279/ A1 - Indik, Julia H. A1 - Marcus, Frank I. Y1 - 2003/07// N2 - Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by the patchy replacement of myocardium by fatty or fibrofatty tissue. These changes lead to structural abnormalities including right ventricular enlargement and wall motion abnormalities that can be detected by echocardiography, angiography, and cine MRI. ARVC/D is a genetically heterogeneous disorder, since it has been linked to several chromosomal loci. Myocarditis may also be a contributing etiological factor. Patients are typically diagnosed during adolescence or young adulthood. Presenting symptoms are generally related to ventricular arrhythmias. Concern for the risk of sudden cardiac death may lead to the implantation of an intracardiac defibrillator. An ongoing multicenter international registry should further our understanding of this disease. PB - Indian Pacing and Electrophysiology Group KW - Arrhythmogenic right ventricular cardiomyopathy TI - Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia SP - 148 AV - public EP - 156 ER -