%A Berardo Sarubbi %A Pasquale Vergara %A Michele D?Alto %A Raffaele Calabr? %J Indian Pacing and Electrophysiology Journal %T Congenital Junctional Ectopic Tachycardia: Presentation And Outcome %X Junctional ectopic tachycardia (JET) is a rare type of supraventricular arrhythmia. Even if its management has improved in recent years, it remains a great challenge for the cardiologist. Two are the possible clinical presentations of this arrhythmia: as a primary idiopathic disorder during infancy, configuring the so called ?congenital? JET, or more often as a transient phenomenon immediately after surgery for congenital heart disease, giving rise to the ?post-operative? variety. The congenital form, firstly described as a distinct entity by Coumel et al. in 19761, usually occurs in the first six months of life presenting as a persistent sustained form, lasting up to 90% of the time. Its clinical presentation may be dramatic, being associated in up to 60% of cases with cardiomegaly and/or heart failure. Congenital JET is hampered by high mortality. Secondary dilated cardiomyopathy, ventricular fibrillation and sudden cardiac death have also been reported 2,3. %N 3 %K Junctional Ectopic Tachycardia, Congenital %P 143-147 %E Balbir Singh %E Yash Lokhandwala %E Johnson Francis %E Anup Gupta %V 3 %D 2003 %I Indian Pacing and Electrophysiology Group %L cogprints4278