http://cogprints.org/4278/
Congenital Junctional Ectopic Tachycardia: Presentation And Outcome
Junctional ectopic tachycardia (JET) is a rare type of supraventricular arrhythmia. Even if its management has improved in recent years, it remains a great challenge for the cardiologist. Two are the possible clinical presentations of this arrhythmia: as a primary idiopathic disorder during infancy, configuring the so called “congenital” JET, or more often as a transient phenomenon immediately after surgery for congenital heart disease, giving rise to the “post-operative” variety.
The congenital form, firstly described as a distinct entity by Coumel et al. in 19761, usually occurs in the first six months of life presenting as a persistent sustained form, lasting up to 90% of the time. Its clinical presentation may be dramatic, being associated in up to 60% of cases with cardiomegaly and/or heart failure.
Congenital JET is hampered by high mortality. Secondary dilated cardiomyopathy, ventricular fibrillation and sudden cardiac death have also been reported 2,3.
Sarubbi, Berardo
Vergara, Pasquale
D’Alto, Michele
Calabrò, Raffaele
Indian Pacing and Electrophysiology Journal
Berardo
Sarubbi
Pasquale
Vergara
Michele
D’Alto
Raffaele
Calabrò